Ruptured Jejunal Gastrointestinal Stromal Tumor- An Unusual Presentation of a Rare Tumor

Aim: We report an extremely rare case of jejunal GIST presenting with acute abdomen and shock due to tumor rupture with hemorrhage.

Case Presentation: A 52 year male presented to the surgical emergency with complaints of acute onset abdominal pain and abdominal distention for 12 hours. On abdominal examination, there was a tender ill defined lump in the umbilical region associated with free fluid. Hemoglobin was 5.4 gm/dl. Ultrasound guided diagnostic peritoneal aspiration revealed blood. Patient underwent exploratory laparotomy with resection and anastomosis of the jejunal segment containing GIST.

Discussion: GISTs (Gastrointestinal stromal tumors) are one of the rare tumors of the gastrointestinal tract. Jejunum is less common site for the origin of GIST accounting for <10% of all gastrointestinal tumors. Ruptured small intestinal GIST is an extremely rare cause of acute abdomen.

Conclusion: The above case report is a very atypical scenario of small bowel GIST presenting with an acute abdomen. Early operative intervention is required to control bleeding and to prevent sepsis in cases of ruptured GIST.